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Nutrition Information

Following a low protein diet is a key part of living with Tyrosinemia Type 1

Published medical guidelines recommend patients with Tyrosinemia Type 1 follow a low-protein diet to avoid complications associated with elevated plasma tyrosine levels.1 However, eating properly while following a low-protein diet can be challenging. The following may help, just remember to always follow your dietitian’s advice:

  • Carefully monitor the intake of natural protein
  • Take medical food/formula as you have been advised
  • If you have any questions, check with your dietitian
  • Consider a food diary or app to help your dietitian better understand your response

It also helps to plan your meals in advance

  • Make it fun. Be inventive, find and create your own recipes

Generally, a low protein diet means:

  • eating vegetables, fruit and low-protein manufactured products;
  • moderating starches e.g., pasta, rice and potatoes; and
  • avoiding meat, fish, soya, nuts and dairy products.

References: 1.Chinsky JM, Singh R, Ficicioglu C, van Karnebeek CDM, Grompe M, Mitchell G, Waisbren S, Gucsavas-Calikoglu M, Wasserstein MP, Coakley K, Scott CR, Diagnosis and treatment of tyrosinemia type I: a US and Canadian consensus group review and recommendations. Genet Med. 2017 Dec;19(12):1-16. doi: 10.1038/gim.2017.101


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