Healthcare professionals and dieticans will recommend a special, controlled diet - along with medication like NITYR (nitisinone) Tablets – to help children, young adults and adults thrive while living with Hereditary Tyrosinemia Type 1 (HT-1).
A low protein diet individualized for each person with HT-1 is essential. Your healthcare professional and metabolic dietician (an expert in nutritional support for those with HT-1 and other amino acid disorders) can help. They often recommend protein substitutes and supplements based on a patient’s age and dietary needs to help meet their protein requirements. Patients with HT-1 have a highly restricted diet in tyrosine and phenylalanine – amino acids that are present in almost all natural protein sources, such as meat, fish and cheese. Protein requirements instead need to be met from supplements made from alternative proteins like GMP, which is a whole protein derived from whey and does not contain tyrosine or phenylalanine.